Isolated pulmonary artery stenosis
isolated stenosis (narrowing) of the pulmonary artery is one of common congenital heart defects and is 6,8-9% of all heart defects.This pathology is equally common in boys and girls.The first description of the defect relates to the 1749
If there is an obstacle release blood from the right ventricle, the pressure in it at the time of contraction (systole) significantly increased (up to 200 mm Hg. Art.).This results in a pressure difference between the right ventricle and the pulmonary artery that ensures the safety of the blood discharge into the pulmonary circulation.In children with severe stenosis of the pulmonary artery of the isolated right atrial pressure rises.Against the backdrop of increased pressure in the right atrium expands the oval window, and reset the "waste" of blood occurs in the left ventricle, ie. E. In the systemic circulation.The amount of blood discharge determines the severity of bluish color of the skin (from crimson to dark blue).
Features manifestations of isolated stenosis
additional child survey methods are an electrocardiogram, chest X-ray, cardiac catheterization and angiocardiography cavities (in doubtful cases).
Indications for surgical treatment of isolated pulmonary artery stenosis at an early age are expressed bluish coloration of the skin, cardiac enlargement, heart failure, the pressure difference between the right ventricle and the pulmonary artery over 40 mmHg.Art.