Common arterial trunk

August 12, 2017 17:51 | Genetic Diseases

Common arterial trunk - it is one large vessel, which departs from the heart through a single valve and provides the coronary (heart) blood flow and the blood from entering the two (large and small) circulation.Other names: common trunk, persistent arterial trunk.The first description of the defect relates to the heart of 1864, total arterial trunk incidence is 2-3% of all congenital heart defects.

In emerging manifestations of children with this defect are reminiscent of patients with ventricular septal defect:. Significant lag in physical development, repeated pneumonia, etc. The leading symptom is shortness of breath quickening in 50-100 minutes.In cases of reduced blood flow through the lungs is significantly reduced breathlessness.Cyanosis of the skin with a total arterial trunk is different: it is minimal or absent with increased pulmonary blood flow, pronounced with a minimum of blood filling of the pulmonary circulation.In the latter cases, cyanosis is accompanied by deformation of the nail on t

he "hour glass" type, and the fingers of the type "drumsticks."On examination in cases of increase in heart size noteworthy forming a heart hump.When auscultation of the heart reveals the characteristic noise.

Additional methods of examination of the child include ECG, PCG (graphic check heart sounds), chest X-ray, ultrasound of the heart.Crucial in the diagnosis of tetralogy of Fallot have a catheterization of heart cavities and angiocardiography.

flow blemish hard from the first days of life due to severe heart failure and overflow blood of the pulmonary circulation.Cyanosis of the skin is determined by the degree of oxygen deficiency in the blood.Most children die in the first months of life, and only 20% survive the first year, and 10% survive to 2-3-th decade.

Cardiac glycosides (digoxin) and diuretics gives only a negligible effect.It recommended an operation to correct the defect.However, the mortality of the operation at an early age is over 70%.In this regard, some clinicians suggest to perform this operation only when the defect appeared accidental discovery on the operating table.