Corrected transposition of the great vessels

August 12, 2017 17:51 | Genetic Diseases

Corrected transposition of the great vessels is a rare congenital heart disease.According to the pathologists, its rate is 0.4-1.2% of all congenital heart defects.However, manifestations of corrected transposition of the great vessels of the minimum, and in many cases remain undiagnosed.For the first time this defect was described in 1956

Corrected transposition of the great vessels may be encountered in the normal and the abnormal position of the heart.In this case the right ventricle with tricuspid valve is located on the left, it circulates arterial (oxygen-rich) blood, and he leaves the aorta, which occupies the left-hand position.The left ventricle with the bicuspid valve is found on the right, it receives deoxygenated ( "Waste") blood, which is directed into the pulmonary artery to the right of the aorta.Often, other congenital heart defects with corrected transposition of the great vessels not, but they can be represented by ventricular septal defect, pulmonary stenosis, at least -. Atrial se

ptal defect, Ebstein's anomaly, etc. coupled with the absence of the spleen is possible.For corrected transposition of the great vessels is characterized by abnormal development of the cardiac conduction system, which provides the appearance of this body of electrical impulses by which there is a reduction of the heart muscle.Circulation with corrected transposition of the great vessels without concomitant congenital heart disease has no features other than arising from the age of arterial insufficiency of left-hand (tricuspid) valve, which is not adapted to function in conditions of high pressure.Of great importance is the functional state of the myocardium of the right (located on the left) ventricle because it pumps blood into the systemic circulation.

No complaints associated congenital heart defects in children and for no blemish favorable.In all other vices arise manifestations are determined by their character and not very different from those defects in the normal position of the ventricles and blood vessels.Children complain of fatigue, shortness of breath, palpitations.Attacks palpitations and discovered the blockade is often mistaken for the consequences of myocarditis (inflammation of the heart muscle).All the noise that determines the physician on auscultation of the heart reflect the associated heart defects.

Suspected corrected transposition of the great vessels to help the ECG data.Additional tests are chest X-ray, ultrasound of the heart, sensing of the heart cavities, angiocardiography.

Surgical treatment of complicated vice aims to correct concomitant vices or prosthetic aortic valve in cases of severe deficiency.